Advertisement
Original communication| Volume 69, ISSUE 2, P208-214, February 1971

Omphalocele—an appraisal of therapeutic approaches

      This paper is only available as a PDF. To read, Please Download here.

      Abstract

      • 1.
        1. Fifty-four cases of omphalocele and gastroschisis are reviewed—the experience at the Red Cross War Memorial Children's Hospital since its opening.
      • 2.
        2. Gastroschisis of necessity is treated operatively, and of 7 cases 3 survived.
      • 3.
        3. Primary operative repair was used in 25 babies with omphalocele and 16 (64 percent) survived.
      • 4.
        4. Of the nine deaths in operative patients, seven were the direct result of excessive intra-abdominal pressure attendant upon replacement of the viscera within the abdominal cavity. This problem was not solved by using skin coverage alone as a first-stage procedure.
      • 5.
        5. Fifteen babies were treated nonoperatively. In 13, this was carried to completion. In two, the method was abandoned because of the development of intestinal obstruction within the sac. One of these latter died. Total survival in the group was 14 (93 percent).
      • 6.
        6. Seven babies were not treated, having died of other problems within the first 24 hours of life.
      • 7.
        7. Problems of nonoperative management are discussed.
      • 8.
        8. The surgical importance of the “omphalocele — macroglossia” syndrome is pointed out.
      • 9.
        9. Our recommendations for management of this condition are listed.
      To read this article in full you will need to make a payment

      Purchase one-time access:

      Academic & Personal: 24 hour online accessCorporate R&D Professionals: 24 hour online access
      One-time access price info
      • For academic or personal research use, select 'Academic and Personal'
      • For corporate R&D use, select 'Corporate R&D Professionals'

      Subscribe:

      Subscribe to Surgery
      Already a print subscriber? Claim online access
      Already an online subscriber? Sign in
      Institutional Access: Sign in to ScienceDirect

      References

        • Ahlfeld F.
        Mschr. Geburtsch. Gynäk. 1899; 10: 124
        • Aitken J.
        Exomphalos. Analysis of a 10-year series of 32 cases.
        Arch. Dis. Child. 1963; 38: 126
      1. Beck, J.: Personal communication.

        • Beckwith J.B.
        • et al.
        Hyperplastic fetal visceromegaly with macroglossia, omphalocele, cytomegaly of adrenal fetal cortex, post natal somatic gigantism, and other abnormalities. Newly recognized syndrome.
        in: Proceedings of The American Pediatric Society, Seattle, Washingtoned. 3. Abst. No. 41. June 16 to 18, 1964
        • Bernstein P.
        Gastroschisis, a rare teratological condition in the newborn.
        Arch. Pediat. 1940; 57: 505
        • Combs J.T.
        • Grunt J.A.
        • Brandt K.A.
        New syndrome of neonatal hypoglycemia. Association with visceromegaly, macroglossia, microcephaly, and abnormal umbilicus.
        New Eng. J. Med. 1966; 275: 236
        • Cunningham A.N.
        Exomphalos.
        Arch. Dis. Child. 1956; 31: 144
        • Drescher E.
        Observations on the conservative treatment of exomphalos.
        Arch. Dis. Child. 1963; 38: 135
        • Eckstein H.B.
        Exomphalos, a review of 100 cases.
        Brit. J. Surg. 1963; 50: 405
        • Grob M.
        Conservative treatment of exomphalos.
        Arch. Dis. Child. 1963; 38: 148
        • Grob M.
        ed. 3. Lehrbuch der Kinderchirurgie. George Thieme Verlag, Stuttgart1957
        • Gross R.E.
        A new method for surgical treatment of large omphaloceles.
        Surgery. 1948; 24: 277
        • Gross R.E.
        The surgery of infancy and childhood.
        W. B. Saunders Company, Philadelphia1953
        • Irving I.M.
        Exomphalos with macroglossia: A study of eleven cases.
        J. Pediat. Surg. 1967; 2: 499
        • Jones P.
        Exomphalos, a review of 45 cases.
        Arch. Dis. Child. 1963; 38: 180
      2. Kiesewetter, W.: Personal communication.

        • Kling S.
        Massive omphalocele: A method of treatment employing skin allograft.
        Canad. J. Surg. 1967; 10: 455
        • Moore T.C.
        Gastroschisis with antenatal evisceration of intestines and urinary bladder.
        Ann. Surg. 1963; 158: 263
        • Moore T.C.
        Gastroschisis—report of two cases treated by a modification of the Gross operation for omphalocele.
        Surgery. 1953; 33: 112
        • Pohl V.
        • Schnierer M.
        Analysis of experience in the therapy of omphalocoele over the period of the last 15 years.
        Cesk. Pediat. 1966; 21: 426
        • Schuster Samuel R.
        A new method for the staged repair of large omphalocoeles.
        Surg. Gynec. Obstet. 1967; 125: 837
        • Simpson T.E.
        • Lynn H.B.
        Omphalocele. Results of surgical treatment.
        in: ed. 3. Mayo Clin. Proc. 43. 1968: 65
        • Slim M.S.
        Combined treatment of omphalocele.
        Surgery. 1967; 61: 314
        • Soave F.
        Conservative treatment of giant omphalocele.
        Arch. Dis. Child. 1963; 38: 130
        • Welch K.J.
        The use of a homograft in the surgical treatment of large omphaloceles.
        Surgery. 1951; 29: 100
        • Wiedeman H.R.
        Complexe malformatif familial avec hernie ombilicale et macroglossie—un “syndrome nouveau”?.
        J. Génét Hum. 1964; 13: 223
        • Wollenweber E.J.
        • Coe H.E.
        Conservative management of eventration in the newborn with survival.
        Amer. J. Surg. 1959; 97: 769
        • Wyburn G.M.
        Congenital defects of the anterior abdominal wall.
        Brit. J. Surg. 1953; 40: 553